Intestinal ischemia due to intestinal malrotation in an adolescent
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Abstract
Background: Intestinal malrotation is a congenital malformation defined as a failure in the rotation and fixation of the intestine during embryogenesis. This pathology is traditionally diagnosed in childhood. However, people with this intestinal malformation may remain asymptomatic for several years of life and manifest, in adolescence or adulthood, chronic and non-specific symptoms, such as intermittent abdominal pain, nausea, and emesis. In the worst cases, in this group of individuals, intestinal malrotation can manifest as an acute volvulus of the midgut, with vascular compromise and intestinal ischemia, which could require extensive resection with the subsequent risk of developing short intestine syndrome, intestinal failure, and even death. Case report: we present the case of a fifteen-year-old girl with an unknown history of congenital intestinal malrotation, which manifested as an acute volvulus with intestinal ischemia that required massive intestinal resection. Intestinal transplantation was the proposed therapeutic option in the face of irreversible intestinal failure and the complications associated with chronic parenteral nutrition. Conclusions: An adolescent's diagnosis of intestinal malrotation requires a high clinical suspicion. It is a clinical challenge since, if it is not identified in time, it can have catastrophic consequences for the life of the patient and her family. Intestinal ischemia due to intestinal malrotation in an adolescent.
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