Right congenital diaphragmatic hernia: report of a successful case treated by thoracoscopy.

Main Article Content

Luis Alejandro Garcia Rairan
Maria Angelica Gonzalez Cruz
Alejandra Alfonso Diaz
Maria Cristina Angulo
Sebastian Silva
Andres Mauricio Delgado

Abstract

Background: Congenital Diaphragmatic Hernia is a rare anatomical defect of the diaphragm that results from the absence or underdevelopment of part or all of the diaphragmatic dome. This leads to the herniation of abdominal organs into the thoracic cavity, causing serious pulmonary and cardiac complications in newborns.


Case Report: We present the case of a 37-week-old newborn with a prenatal history of congenital heart disease, suspected aortic coarctation, and abnormal middle cerebral artery Doppler. Within minutes of birth, the newborn experienced ventilatory failure, necessitating ventilatory support. Additionally, a chest X-ray revealed abdominal viscera in the right hemithorax, raising suspicion of Right Congenital Diaphragmatic Hernia, which was subsequently confirmed by ultrasound. The newborn underwent thoracoscopy to correct the diaphragmatic defect, achieving complete correction of the hernia without complications and an adequate postoperative recovery. Discharge occurred within a few days of hospitalization.


Conclusion: We recommend early diagnosis and delivery in specialized centers with a higher level of care to increase the chances of survival.

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How to Cite
Garcia Rairan, L. A., Gonzalez Cruz, M. A., Alfonso Diaz, A., Angulo, M. C., Silva, S., & Delgado, A. M. (2023). Right congenital diaphragmatic hernia: report of a successful case treated by thoracoscopy. Pediatría, 56(3), e438. https://doi.org/10.14295/rp.v56i3.438
Section
Case report
Author Biographies

Maria Angelica Gonzalez Cruz, 4. Facultad de Medicina. Universidad El Bosque. Bogotá, Colombia

Medica con participación en la investigación de la industria farmaceutica.

Alejandra Alfonso Diaz, 4. Facultad de Medicina. Universidad El Bosque. Bogotá, Colombia

Médico. Departamento de Urgencias y Hospitalización. Hospital Central de la Policía. Bogotá, Colombia

Maria Cristina Angulo, Pediatra Fundación Santa fe de Bogotá

Pediatra, Miembro institucional Fundación Santa Fe de Bogotá, Profesor clínico Universidad de los Andes

Sebastian Silva, Médico. Departamento de Hospitalización. Clínica Palermo. Bogotá, Colombia.

Médico. Departamento de Hospitalización. Clínica Palermo. Bogotá, Colombia.

Andres Mauricio Delgado, Pediatra. Hospital San Rafael

Pediatra, Hospital Universitario Clínica San Rafael, Profesor clínico Universidad Militar Nueva Granada, Universidad de la Sabana.

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