Necrotizing pancreatitis as an atypical presentation of cystic fibrosis in a preschool patient
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Abstract
Background: Cystic fibrosis is a disease with autosomal recessive inheritance, consisting of mutations in the transmembrane conductivity regulatory gene, causing an alteration in the viscosity of secretions. Case report: We present the case of a preschool patient admitted due to chronic abdominal pain who was diagnosed with necrotizing pancreatitis as a cystic fibrosis debut, requiring four months of hospitalization. Conclusion: Cystic fibrosis is a disease with a high morbidity and mortality rate in the pediatric population; physicians should know its possible debut forms and clinical presentation for timely management and interdisciplinary follow-up.
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